Congenital extradural spinal cysts are exceedingly rare and represent the least common cause of spinal cord pressure. The literature records only 35 cases. This fact, coupled with the satisfying surgical results, dictates the periodic review and discussion of the symptoms and diagnostic features. These extradural cysts have a high predilection for the thoracic region, 29 of the 35 reported cysts occurring entirely within the thoracic region. Six have been reported extending into the lumbar region, and of these only two have occurred isolatedly in the lumbar area.
The literature is consistent in reporting the symptomatology and signs of spinal extradural cysts as being compatible with an expanding lesion in the thoracic area. This description was initiated by Elsberg, in 1934, and has been quoted verbatim in several of the subsequent reports as follows:
The individual is an adolescent with the history and symptoms of a progressive spastic paraplegia. Pain is
SMITH GW, CHAVEZ M. Lumbar Extradural Cysts—CongenitalTheir Proper Classification. AMA Arch NeurPsych. 1958;80(4):436-440. doi:10.1001/archneurpsyc.1958.02340100036005