ANGIOCARDIOGRAPHY permits the diagnosis of congenital absence of a main branch of the pulmonary artery during life. The first patient with congenital absence of a right pulmonary artery had angiocardiography at Cornell Medical Center in 1948, and was reported in 1953.1 The first publication on this subject after using angiocardiography, however, was made by Madoff and associates2 in 1952.
Recent reviews indicate that there are now well over 100 cases of congenital absence of a pulmonary artery in the literature.3-10 Whereas, congenital absence of the right pulmonary artery is often isolated and uncomplicated, congenital absence of the left pulmonary artery is frequently accompanied by other congenital cardiovascular anomalies.3 In this report, congenital absence of the left pulmonary artery associated with a right aortic arch and patent right- and left-sided ductus arteriosus is described. Treatment consisted of ligation and division of the ductus, and left pneumonectomy.
Steinberg I, Miscall L, Goldberg HP. Congenital Absence of Left Pulmonary Artery With Patent Ductus ArteriosiTreatment by Closure of Ductus and Left Pneumonectomy. JAMA. 1964;190(4):394–396. doi:10.1001/jama.1964.03070170135028