PNEUMATOSIS cystoides intestinalis (PCI) is an entity characterized by numerous submucosal or subserosal collections of air-filled cysts in the intestinal tract. This disorder has been described in association with a variety of gastrointestinal (GI) diseases: pyloric stenosis, esophageal stricture, diaphragmatic hernia, inflammatory and obstructive bowel disease, tuberculous enteritis, intestinal neoplasia, For editorial comment see p 1965. and scleroderma, as well as obstructive pulmonary diseases and coughing.1 More recently PCI has been noted following blunt abdominal trauma2 and jejunoileal bypass.3 Herein we report a patient with PCI in association with acquired megacolon.4 To our knowledge, this association has not been previously described.
Report of a Case
A 57-year-old resident of the state mental institution was first admitted to our hospital in November 1974 with abdominal distention, a 7-kg weight loss, and occasional clay-colored stools. A duodenal biopsy specimen revealed chronic inflammation in the lamina propria with no
Broecker BH, Moore EE. Pneumoperitoneum Due to Pneumatosis Cystoides Intestinalis in Idiopathic Megacolon. JAMA. 1977;237(18):1963. doi:10.1001/jama.1977.03270450053021