The biopsy specimen showed sheets of uniform spindled cells in the dermis interlacing in a storiform or cartwheel pattern. The cells invaded the subcutaneous fat, extending between the cells in a honeycomb pattern. Other subcutaneous areas showed multiple layers of spindle cells oriented parallel to the skin surface.
The patient was referred for Mohs micrographic surgery, and the margins were cleared after debulking and 1 stage.
Dermatofibrosarcoma protuberans is a low-grade fibrosarcoma.1 It is a rare tumor, with an estimated incidence of anywhere from 0.8 to 5 cases per 1 million persons in the general population.2,3 In a university study of 132 black patients with skin cancer, 16 (12.1%) were diagnosed as having DFSP.4
Slowly Expanding Abdominal Plaque. Arch Dermatol. 1998;134(11):1477-1482. doi: