Prurigo pigmentosa (PP) is a rare acquired inflammatory dermatosis with peculiar clinical and histological features. The disease, which predominantly occurs in young women, has been most frequently reported in Japan. In a review of the literature, we found only a few cases of PP in non-Japanese patients compared with more than 300 in Japanese patients.1 Although ethnicity and environmental factors have been claimed to play a role in the pathogenesis of PP, so far no cause has been identified for this striking eruption. We describe monozygotic white twins who both developed PP.
Houriet C, Perruchoud DL, Beltraminelli H, Borradori L. Prurigo Pigmentosa in White Monozygotic Twins. JAMA Dermatol. 2017;153(3):353-354. doi:10.1001/jamadermatol.2016.4921