A 67-year-old woman with biopsy-proven cicatricial pemphigoid had bilateral cicatricial entropion and trichiasis leading to blindness in the right eye and severe visual impairment in the left eye. This occurred despite treatment that included methylprednisolone, prednisolone, methotrexate, cyclosporine, dapsone, mycophenolate mofetil, intravenous immunoglobulins, and plasma exchange. In the hope of rescuing her sight, she was referred for an osteo-odonto-keratoprosthesis (OOKP) for her right eye.
Langan EA, Liu C, Ogden S, Griffiths CEM. A Tooth for an Eye: Cicatricial Pemphigoid and the Osteo-Odonto-Keratoprosthesis. Arch Dermatol. 2010;146(10):1188-1189. doi:10.1001/archdermatol.2010.277