Microcystic adnexal carcinoma (MAC) also known as sclerosing sweat duct carcinoma, is a rare cutaneous neoplasm with ductal and follicular components that is locally aggressive.1,2 It usually occurs in adults, most frequently on the head and neck.2 The diagnosis is made histopathologically, and the differential diagnosis includes syringoma and desmoplastic trichoepithelioma. We describe herein the first congenital MAC to our knowledge.
Fu T, Clark FL, Lorenz HP, Bruckner AL. Congenital Microcystic Adnexal Carcinoma. Arch Dermatol. 2011;147(2):256-257. doi:10.1001/archdermatol.2010.440