February 1999

Ichthyosis Bullosa of Siemens: A Topical Therapy Option

Author Affiliations

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Copyright 1999 American Medical Association. All Rights Reserved. Applicable FARS/DFARS Restrictions Apply to Government Use.1999

Arch Dermatol. 1999;135(2):217-218. doi:10-1001/pubs.Arch Dermatol.-ISSN-0003-987x-135-2-dlt0299

Ichthyosis bullosa of Siemens (IBS) is a dominant autosomal disease characterized by the absence of congenital erythroderma and mild blistering explained by the superficial location of epidermolytic hyperkeratosis (granulous and superficial spinous layers). In addition, IBS involves gray hyperkeratosis in elbows, knees, and other denuded areas with normal skin at the base (molting or Mauserung phenomenon).1,2

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