Pityriasis rubra pilaris (PRP) is a rare papulosquamous disorder of unknown origin. Although PRP usually resolves within 1 to 3 years,1 treatment of the disease is generally difficult. Encouraged by good results with extracorporeal photochemotherapy (ECP) in patients with erythroderma of other origin,2- 4 we treated 2 patients with erythrodermic PRP type I using ECP in combination with systemic retinoids and cyclosporine, respectively.
Hofer A, Müllegger R, Kerl H, Wolf P. Extracorporeal Photochemotherapy for the Treatment of Erythrodermic Pityriasis Rubra Pilaris. Arch Dermatol. 1999;135(4):475-476. doi:10-1001/pubs.Arch Dermatol.-ISSN-0003-987x-135-4-dlt0499