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Incontinentia Pigmentia. Presented by Charles George Steffen, MD.
The patient is a 19-year-old girl whose mother first noticed a vague increase in pigmentation of her daughter's skin at the age of 6 weeks. There were no previous blisters nor inflammation.When the patient was approximately 1 year of age, the mother noticed some increased pigmentation on the forehead which gradually became worse.At approximately the age of 5, scaling and erythematous patches appeared on the scalp which were thought to be seborrhea. Gradually, the scaling and the erythema disappeared leaving a partial alopecia and atrophy.The patient has had surgery for the repair of a patent ductus arteriosus and has had a congenital dislocated hip and clubfoot. Her intelligence is normal. She is a student in college.
There are linear areas of increased pigmentation (freckling), particularly over the right side of the trunk, right arm,
Linden IH, Carney JW, Williamson C, Ayres S. THE LOS ANGELES DERMATOLOGICAL SOCIETY. Arch Dermatol. 1967;96(3):342-345. doi:10.1001/archderm.1967.01610030120021