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Article
April 1974

Klippel-Trenaunay-Weber Syndrome

Author Affiliations

Vienna, Austria

Arch Dermatol. 1974;109(4):573. doi:10.1001/archderm.1974.01630040077029

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Abstract

To the Editor.—  In the July issue of the Archives (108:111, 1973), Dr. Owens and co-workers discussed the nomenclature of "Klippel-Trenaunay-Weber syndrome." I would like to bring forward some objections:The association of varicose veins, hypertrophy of a limb, and cutaneous hemangiomas of the port-wine type has already been described in some case reports in the 19th century. Klippel and Trenaunay and, seven years later, Parkes-Weber were the first to point this out as a syndrome.In 1918 Parkes-Weber "has not noted the triad to include congenital arteriovenous fistulas," but differentiated a distinctly different syndrome that he called "haemangiectatic hypertrophy of limbs." The typical feature of this syndrome was "a definite kind of thrill or pulsations, rhythmical with the heart's contractions . . . as in cases of arteriovenous anastomosis of traumatic origin."Against this historical background and in view of the fact that, according to Owens et al, the "existence of arteriovenous

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