This article is only available in the PDF format. Download the PDF to view the article, as well as its associated figures and tables.
To the Editor.—
In the July issue of the Archives (108:111, 1973), Dr. Owens and co-workers discussed the nomenclature of "Klippel-Trenaunay-Weber syndrome." I would like to bring forward some objections:The association of varicose veins, hypertrophy of a limb, and cutaneous hemangiomas of the port-wine type has already been described in some case reports in the 19th century. Klippel and Trenaunay and, seven years later, Parkes-Weber were the first to point this out as a syndrome.In 1918 Parkes-Weber "has not noted the triad to include congenital arteriovenous fistulas," but differentiated a distinctly different syndrome that he called "haemangiectatic hypertrophy of limbs." The typical feature of this syndrome was "a definite kind of thrill or pulsations, rhythmical with the heart's contractions . . . as in cases of arteriovenous anastomosis of traumatic origin."Against this historical background and in view of the fact that, according to Owens et al, the "existence of arteriovenous
Partsch H. Klippel-Trenaunay-Weber Syndrome. Arch Dermatol. 1974;109(4):573. doi:10.1001/archderm.1974.01630040077029