The nevus of Ota is a pigmentary disorder that has been associated with nevus flammeus. A patient had nevus of Ota, nevus flammeus, unilateral glaucoma with retinal angiomatosis associated with gastrointestinal hemangiomas and probable Takayasu arteritis, with abdominal coarctation and carotid stenosis. To our knowledge, this Is the first report of such an association.
Reinke RT, Haber K, Josselson A. Ota Nevus, Multiple Hemangiomas, and Takayasu Arteritis. Arch Dermatol. 1974;110(3):447-450. doi:10.1001/archderm.1974.01630090081022