• Multiple fibrous histiocytomas of the dermis (dermatofibromas) were found in six males of one family. A number of the tumors fell within the histologic patterns commonly encountered in dermatofibromas, but some were unusually large and others were cytologically atypical. In addition, the proband died of a malignant fibrous histiocytoma of the lung. We believe that this is a syndrome and a familial variant of a common dermal entity.
(Arch Dermatol 117:12-15, 1981)
Roberts JT, Byrne EH, Rosenthal D. Familial Variant of Dermatofibroma With Malignancy in the Proband. Arch Dermatol. 1981;117(1):12-15. doi:10.1001/archderm.1981.01650010018015