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November 1981

Epidermolysis Bullosa Letalis Associated With Congenital Pyloric Atresia

Author Affiliations

From the Departments of Dermatology (Drs Peltier, Tschen, Raimer, and Kuo) and Pathology (Dr Kuo), University of Texas Medical Branch, Galveston.

Arch Dermatol. 1981;117(11):728-731. doi:10.1001/archderm.1981.01650110050019

• A 32-week-old (gestational age) female infant with epidermolysis bullosa letalis (EBL) (confirmed by light and electron microscopy) had a gastric-outlet obstruction on routine roentgenographic examination. An autopsy showed a fibrous cord connecting the stomach and first part of the duodenum in the area of the pylorus. A review of the literature indicated 12 additional cases of epidermolysis bullosa (EBL where type was confirmed) associated with pyloric atresia. The possibility of coexistent pyloric atresia should be considered in a newborn who has suspected EBL.

(Arch Dermatol 1981,117:728-731)