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April 1982

The Ectodermal Dysplasias

Author Affiliations

Curitiba, Brazil

Arch Dermatol. 1982;118(4):215-216. doi:10.1001/archderm.1982.01650160005006

To the Editor.—  We read the article by Solomon and Keuer in the November 1980 Archives (116:1295-1299) and the article by Hazen et al in the December 1980 Archives (116:1385-1387) on ectodermal dysplasia (ED) and would like to offer some comments to elucidate some topics.Concerning the Solomon and Keuer article, the word "anhidrosis" should not be used to characterize Christ-Siemens-Touraine (CST) syndrome, since these patients are hypohidrotic. Weech1 could not explain why female patients were sometimes found to have CST, an X-linked recessive syndrome, but we now know the reason. They had another condition—autosomal recessive hypohidrotic ED.2-4 The name "Thurnam" was misspelled as "Thurman," and the information that he studied one patient is not correct. He actually studied two first cousins and their maternal grandmother who was identified as a carrier.5 Clouston's syndrome should better be designated the Fischer-Jacobsen-Clouston syndrome to avoid the impression that Fischer and

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