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January 1989

Congenital Ichthyosiform Dermatosis With Linear Keratotic Flexural Papules and Sclerosing Palmoplantar Keratoderma

Author Affiliations

From the Departments of Dermatology (Drs Pujol, Alomar, and de Moragas) and Pathology (Dr Moreno), Hospital Sant Pau, Barcelona, Spain.

Arch Dermatol. 1989;125(1):103-106. doi:10.1001/archderm.1989.01670130105016

• Four members of a consanguineous family showed a congenital disorder characterized by an ichthyosiform dermatosis, sclerosing palmoplantar keratoderma, and multiple keratotic papules arranged in bands with a linear, cordlike distribution. This association seems to represent a distinct entity. The differential diagnosis is described.

(Arch Dermatol 1989;125:103-106)