The blue rubber bleb nevus syndrome (BRBNS) consists of cavernous hemangiomas and hemangiomas of extracutaneous sites, most often gastrointestinal and skeletal.1 We describe a patient with BRBNS who presented with spinal cord compression and vertebral collapse due to vertebral hemangioma. This is the first report of a symptomatic vertebral hemangioma in association with BRBNS.
Report of a Case.
A 50-year-old white man experienced progressive pain and weakness of his legs following a minor back injury. He underwent a routine lumbar decompression with partial relief. However, increased pain and proximal leg weakness developed, and the patient became unable to walk. A total myelogram revealed a highgrade 75% to 80% block at the T4 vertebral level with marked indentation of the dural sac. Computed tomography revealed a destructive honeycomb appearance to the vertebral body and a mass extending into the spinal canal. A gadolinium-enhanced magnetic resonance image showed a large mass
Garen PD, Sahn EE. Spinal Cord Compression in Blue Rubber Bleb Nevus Syndrome. Arch Dermatol. 1994;130(7):934-935. doi:10.1001/archderm.1994.01690070130024