Since the first comprehensive description of ainhum by da Silva Lima in 1880,1 there have been several individual reports of digital constrictions with eventual progression to spontaneous amputation. These conditions were classified by Wells and Robinson2 into 4 classes: (1) ainhum, (2) congenital bands, (3) ainhumlike bands associated with other diseases, and (4) bands secondary to trauma. Neumann3 later used the term pseudoainhum to distinguish the latter 3 categories from the specific entity, ainhum. The term ainhum or dactylolysis spontanea is restricted to spontaneous occurrence of a painful annular constriction predominantly in the fifth toe of the black adult. Various seemingly unrelated disorders have been associated with pseudoainhum. We report a case of pseudoainhum associated with linear scleroderma.
Report of a Case.
A 27-year-old Korean man presented with a history of spontaneous amputation of a digit following progressive tightening of the skin over the left upper limb.
Park BS, Cho KH, Youn JI, Chung JH. Pseudoainhum Associated With Linear Scleroderma. Arch Dermatol. 1996;132(12):1520-1521. doi:10.1001/archderm.1996.03890360114028