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Article
February 1924

LA DÉGÉNÉRESCENCE HÉPATO-LENTICULAIRE.

Arch Intern Med (Chic). 1924;33(2):279. doi:10.1001/archinte.1924.00110260125009

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Abstract

This is the most complete monograph on the subject of lenticular degeneration that has yet appeared. Hall first gives a brief review of Wilson's four cases and a summary of the clinical features of the syndrome called by Wilson "progressive lenticular degeneration." He then correlates the Westphall-Strümpell pseudosclerosis with Wilson's syndrome; he believes that the corneal pigmentation noted in many cases of pseudosclerosis is of frequent occurrence in progressive lenticular degeneration, although it was overlooked by Wilson. He next reports four cases of his own and the histories of three other patients provided by the courtesy of his confréres in Copenhagen. Four of these patients belonged to one family, and two others were brothers. In the review of these seven cases he expresses his opinion that one case was an example of true Wilson's disease; that Cases 2 and 3 were pseudosclerosis, and that Cases 4 to 7 form a

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