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July 1980

Primary Hemochromatosis With Hereditary Spherocytosis

Arch Intern Med. 1980;140(7):983-984. doi:10.1001/archinte.1980.00040020983025

A patient with both hereditary spherocytosis and hemochromatosis is described. At the time of the initial diagnosis of hereditary spherocytosis and shortly after splenectomy, 8 g of iron was removed by phlebotomy. During the next 15 years, the patient continued to accumulate excess iron despite splenectomy-induced remission of the hemolytic disorder. Thus the hemochromatosis in this patient was not secondary to the hereditary spherocytosis but rather represented a primary, ie, genetic abnormality of iron absorption.

(Arch Intern Med 140:983-984, 1980)