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Clinical Notes
November 1968

Muscular Subaortic Stenosis and Coronary Arteriovenous Fistula

Arch Intern Med. 1968;122(5):426-429. doi:10.1001/archinte.1968.00040010426010

Muscular subaortic stenosis (MSS) has been described in association with several congenital cardiovascular anomalies. Previous reports have described this disease in association with persistent atrioventricular (A-V) canal and pulmonary valvular stenosis,1 "parachute mitral valve" with supravalvular ring of the left atrium and coarctation of the aorta,2 ventricular septal defect,3 bicuspid aortic valve,4 and patent ductus arteriosis.5.In addition a syndrome of congenital deafness, hypertelorism, broad nasal root, low set ears, cervicodorsal scoliosis, and hypoplastic fifth digits has been described to occur in association with MSS.6 The present case describes the first patient with MSS and a congenital coronary arteriovenous fistula.