[Skip to Content]
[Skip to Content Landing]
Article
August 1971

PROGRESSIVE LENTICULAR DEGENERATION: A FAMILIAL NERVOUS DISEASE ASSOCIATED WITH CIRRHOSIS OF THE LIVER1

Author Affiliations

Registrar to the National Hospital, Queen Square, London (From the Laboratory of the National Hospital, Queen Square.)

Arch Neurol. 1971;25(2):180-186. doi:10.1001/archneur.1971.00490020098013
Abstract

Introduction  The object of this paper is to give a full description of a rare nervous disease, of which, as far as I am aware, no instance has been recorded during the last twenty years—a disease to which, for reasons which will hereinafter become evident, the name of "Progressive Lenticular Degeneration" may be conveniently applied.... This affection, where it occurs in an uncomplicated form, is an extrapyramidal motor disease, the importance of which is apparent not only because of its rarity, but also by reason of the light it sheds on such diseases as paralysis agitans....Progressive lenticular degeneration, as the disease may be called, is not one with which the medical profession is familiar. As far as I can discover, no case has been recorded since 1890, with the very doubtful exception of one reported by Anton, of Halle, under the title of "Dementia Choreo-asthenica, with Juvenile Nodular Cirrhosis

First Page Preview View Large
First page PDF preview
First page PDF preview
×