Creutzfeldt-Jakob disease (CJD) may present itself with cerebellar symptoms initially. Three cases of our own are presented and the literature has been reviewed. Recognition of CJD presenting with ataxic symptoms is stressed, since such a subform constitutes 10% of all cases of CJD reported to date.
Gomori AJ, Partnow MJ, Horoupian DS, Hirano A. The Ataxic Form of Creutzfeldt-Jakob Disease. Arch Neurol. 1973;29(5):318–323. doi:10.1001/archneur.1973.00490290058006