This 38-year-old woman was born with a cutaneous vascular nevus on the right side of her face and arm. Since infancy, she suffered from medically intractable complex partial seizures. Computed tomography evaluation revealed cortical calcifications (Figure 1) and enlargement of the right choroid plexus (Figure 1). There was right hemisphere cerebral atrophy with associated expansion of the right frontal sinus, thickening of the diploic space, and elevation of the petrous ridge (Figure 2).
Corey SA, O’Donovan CA. Sturge-Weber Syndrome and Accompanying Dyke-Davidoff-Masson Syndrome. Arch Neurol. 2005;62(12):1928-1929. doi:10.1001/archneur.62.12.1928