A 5-year-old boy with Sturge-Weber syndrome (SWS) and glaucoma receiving treatment since infancy elsewhere presented with raised intraocular pressure (IOP) in the right eye. He had undergone trabeculectomy in the right eye with mitomycin C 4 years earlier. On examination, his best-corrected visual acuity was 6/60 (−2.5 diopters sphere/0.5 diopters cylinder × 90) and 6/6 (0.5 diopters sphere) OD and OS, respectively. His IOP was 36 mm Hg and 12 mm Hg OD and OS, respectively, while receiving the maximum-tolerated antiglaucoma medications. Fundus examination was normal (Figure 1A and B), and B-scan ultrasonography revealed no mass lesion in the right eye. The left eye was normal.
Kaushik S, Kaur S, Pandav SS, Gupta A. Intractable Choroidal Effusion With Exudative Retinal Detachment in Sturge-Weber Syndrome. JAMA Ophthalmol. 2014;132(9):1143-1144. doi:10.1001/jamaophthalmol.2014.2464