A 61-year-old man had pain, redness, and decreased motility of the righteye of 2 months' duration. He had undergone excision of a lumbar dermatofibrosarcomaprotuberans (DFSP) 2 years earlier. His visual acuity was hand motions inthe right eye. Examination showed proptosis and severe motility restriction.Computed tomography (Figure 1) andneedle biopsy substantiated the suspicion of metastatic DFSP to the orbit.The patient underwent orbital radiation therapy to reduce pain symptoms. Palliativechemotherapy was given for his multiple concurrent systemic metastases. Ninemonths after initial examination, the patient requested surgical managementbecause of continued discomfort and worsening disfigurement of his orbit (Figure 2).
Nakra T, Cook T, Douglas RS, Goldberg RA. Dermatofibrosarcoma Protuberans Metastatic to the Orbit. Arch Ophthalmol. 2004;122(8):1240-1241. doi:10.1001/archopht.122.8.1240