After a routine appointment with her optometrist, an 11-year-old girl was referred with an unusual fundus appearance. She was visually asymptomatic with no family history of ocular disease. On examination, her visual acuity was 6/5 in each eye. Anterior segment examination results were unremarkable. Fundus examination (Figure) showed a dark clump of pigment at each fovea. There was a bilateral and symmetrical reticular pattern of pigment clumping at the level of the retinal pigment epithelium. Retinal vasculature was of normal caliber, and the optic nerve heads were of normal appearance with good color. Electroretinographic responses were within normal limits.
McGimpsey SJ, Rankin SJA. Case of Sjögren Reticular Dystrophy. Arch Ophthalmol. 2007;125(6):850. doi:10.1001/archopht.125.6.850