Angiomatosis retinae is a relatively rare condition. Many experienced ophthalmologists have never seen it. Bedell1 in 1931 found that less than 100 cases had been reported. Cordes and Hogan2 in 1940 found that the number in the literature had risen to 135. Since that time about 10 additional cases have been reported.3 The first description of the condition was in 1882 by Fuchs,4 who considered it an arteriovenous aneurysm. Wood5 in 1892 and Collins6 in 1894 described the next cases. Von Hippel7 was apparently the first to realize that the disease is a clinical entity, and since his publication in 1904 the condition has been called von Hippel's disease. In 1927 Lindau8 reported that angiomatous tumors of the retina were often part of a general disorder characterized by angiomatous cysts of the cerebellum, medulla, spinal cord, adrenals, kidneys, liver, epididymis and ovaries.
LEWIS PM. ANGIOMATOSIS RETINAEREPORT OF SUCCESSFUL TREATMENT IN ONE CASE. Arch Ophthalmol. 1943;30(2):250–254. doi:10.1001/archopht.1943.00880200098012