DERMATOMYOSITIS is a rare disease of protean manifestations. It is characterized clinically by degeneration of many of the muscles of the body together with a nonsuppurative inflammation and atrophy of the skin and mucous membranes. Involvement of the retina is the rarest manifestation of this rare syndrome. The retinal involvement was first noted by Bruce1 in 1938 in a report of 3 cases, in 1 of which autopsy was performed, with histologic examination of the posterior segment of the eye. The case to be reported represents a second one in which histologic examination of the eye at autopsy was possible.
The disease was first described in 1863 by Wagner.2 It may appear acutely, with severe and rapidly progressive symptoms ; or it may be seen in a subacute or chronic form, with remissions and exacerbations and sometimes complete recovery. In 2 of the 3 cases reported by
LISMAN JV. DERMATOMYOSITIS WITH RETINOPATHYReport of a Case. Arch Ophthalmol. 1947;37(2):155-159. doi:10.1001/archopht.1947.00890220164005