The aortic arch syndrome represents a chronic disorder of the great arteries which branch from the aortic arch, resulting in diminished caliber and insufficient blood supply to the areas supplied by these vessels. Takayasu-Ohnishi's (pulseless) disease is an example of an aortic arch syndrome characterized by diminished or absent pulsation in the arteries of the head, neck, and upper extremities. Pulseless disease in its classic form is rare and it might be well to consider this as a separate entity or syndrome. Some of the aortic arch syndromes may not even have pulselessness, but when it does not exist in a given case, then it is problematic where carotid and vertebral-basilar insufficiency per se ends and the aortic arch syndromes begin.
Takayasu1 in 1908 reported a case which had peculiar, wreath-like anastomoses of the central artery and vein of the retina around the optic disk. Ohnishi, at
HEDGES TR. The Aortic Arch Syndromes. Arch Ophthalmol. 1964;71(1):28-34. doi:10.1001/archopht.1964.00970010044005