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January 1965

Central Areolar Choroidal Dystrophy

Author Affiliations

Bethesda, Md
From the Ophthalmology Branch, National Institute of Neurological Diseases and Blindness, National Institutes of Health, United States Public Health Service, Department of Health, Education and Welfare.

Arch Ophthalmol. 1965;73(1):32-35. doi:10.1001/archopht.1965.00970030034008

Introduction  This rare hereditary retinal dystrophy has not been reported previously in this country, although several reports have appeared in the British and European literature.1-7 The name "central senile areolar choroidal atrophy" was appended to the disorder in 1884 by Nettleship1 who first described this entity; and other authors,4,5,8 on the basis of the clinical picture, have used the term "central areolar choroidal sclerosis." However, the genetic nature of the disorder and the absence of a circumscribed sclerosis of the choroidal vessels make the term "central areolar choroidal dystrophy" preferable.

Report of Cases 

Case 1 (Fig 1 and 2).  —This 57-year-old white female, the mother of patients 2 and 3, has had a bilateral decrease in visual acuity since age 14. This was of very rapid onset, and there was no progression of the symptoms after age 20. She prefers a darkened environment for good visual acuity.

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