Trichoepithelioma is an uncommon, benign, often multiple tumor of the skin which is frequently hereditary and usually begins during puberty. Although many cases are somewhat cosmetically disfiguring, they usually result in no other physical handicap. The case presented here demonstrates a most severe form of the disease in which the patient's already compromised vision was further reduced by the physical obstruction from the large tumors.
Report of Case
This 67-year-old white female first noted the occurrence of small multiple skin tumors on her face, neck, back, and ears about the age of 12 years. These slowly increased in size and number during her life, but not until the past 15 years did these tumors become large enough to become quite disfiguring. She was first seen at the Oklahoma University Medical Center in 1952 at which time clinical diagnoses of lepromatous leprosy or diffuse neurofibromatosis were considered. However, on histopathologic examination
BISHOP DW. Trichoepithelioma. Arch Ophthalmol. 1965;74(1):4-8. doi:10.1001/archopht.1965.00970040006003