Since the first complete description1,2 of a rare syndrome of posterior embryotoxon, abnormal tissue in the angle of the anterior chamber, hypoplasia of the anterior stromal layer of the iris, pupil anomalies, and secondary glaucoma (Rieger's syndrome, mesostromal dysgenesis of cornea and iris) a number of cases have been reported.3 Here we report another case, remarkable because of its association with secondary glaucoma of an unusual type.
Report of a Case
The patient, a 19-year-old girl, was admitted to the University Eye Clinic of Amsterdam in July 1963. Both eyes presented the complete picture of Rieger's anomaly: posterior embryotoxon, marked hypoplasia of the stromal layer of the iris, displaced and distorted pupils, and strands of tissue running from the trabeculae of the iris to the posterior surface of the cornea (Fig 1). Gonioscopy revealed that the angle of the anterior chamber in both eyes was filled with a
BREEBAART AC. A Case of Rieger's Anomaly With Glaucoma—Influence of Sleep. Arch Ophthalmol. 1966;76(6):825-828. doi:10.1001/archopht.1966.03850010827008