The most prominent feature of this case was a large, ring-shaped, nonpigmented mass that occupied almost the entire limbus. Neither the clinical nor the gross examination of the enucleated eye, including the use of a dissecting microscope, aided in making the correct diagnosis. Microscopic examination revealed the limbal mass to be an extra-scleral extension of an extremely diffuse malignant melanoma of the uvea.
The unique appearance of this limbal extension from an uncommon form of malignant melanoma prompted this case report.
Report of Case
A 70-year-old man had been seen one year prior to enucleation, with a one-month history of a blind, painful eye. At that time he had refused enucleation. When he returned with the same complaints, the examination revealed a large, elevated, doughnutshaped limbal mass. This lesion had not been noted previously. In addition corneal edema, a heavy aqueous flare, posterior synechiae, a mature cataract, and secondary
SPAULDING AG, GREEN WR, FONT RL. Ring-Shaped Limbal TumorSecondary to Unrecognized Diffuse Malignant Melanoma of the Uvea. Arch Ophthalmol. 1967;77(1):76-80. doi:10.1001/archopht.1967.00980020078016