A case history and description of the ocular and systemic findings in a patient with malignant atrophic papulosis of Degos is presented, and the known cases of this disease are summarized. An etiologic diagnosis could not be made. A surprisingly high incidence of eye lesions is observed in this rare disease.
Howard RO, Klaus SN, Savin RC, Fenton R. Malignant Atrophic Papulosis (Degos' Syndrome). Arch Ophthalmol. 1968;79(3):262-271. doi:10.1001/archopht.1968.03850040264007