A patient is presented with a congenital, external, unilateral oculomotor nerve palsy associated with the nevus sebaceous of Jadassohn. The nevus sebaceous of Jadassohn frequently has malignant potential and can be the presenting manifestation of a neurocutaneous syndrome. The ocular abnormalities of the syndrome are reviewed. Attention is called to features which overlap those of the oculoauriculovertebral dysplasia of Goldenhar.
Haslam RHA, Wirtschafter JD. Unilateral External Oculomotor Nerve Palsy and Nevus Sebaceous of Jadassohn. Arch Ophthalmol. 1972;87(3):293-300. doi:10.1001/archopht.1972.01000020295012