The principal characteristics of achromatopsia are complete color blindness, subnormal vision, and severe photophobia. It is usually a recessive hereditary trait. The visual acuity of 80% of the patients studied ranged from 20/280 to 20/100. The incidence of strong refractive errors ranged from 4.50 to 10.00 D in 38% of the patients. Reading additions of +4.00 to +16.00 D were prescribed in 13 cases, and 94% of the prescriptions were judged to be successful. Severe photophobia was mitigated by lenses that transmit 19% of the visible spectrum. Followup showed that the majority of the children were able to read regular type in a normal educational setting, and none had to resort to reading large type or braille.
Fonda G, Thomas H. Correction of Low Visual Acuity in AchromatopsiaUse of Corrective Lenses as an Aid to Educational and Vocational Placement. Arch Ophthalmol. 1974;91(1):20-23. doi:10.1001/archopht.1974.03900060024006