• Two patients with orbital vascular malformation and ipsilateral facial nevus flammeus were studied. The literature contains one similar case that interestingly shares with our cases the lack of leptomeningeal angiomatosis. Orbitofacial angiomatosis seems to be a distinct entity from meningofacial angiomatosis because of its true vascular malformation of the orbit.
Hofeldt AJ, Zaret CR, Jakobiec FA, Behrens MM, Jones IS. Orbitofacial Angiomatosis. Arch Ophthalmol. 1979;97(3):484-488. doi:10.1001/archopht.1979.01020010234009