December 1986

Apocrine Hidrocystomas of the Lids, Hypodontia, Palmar-Plantar Hyperkeratosis, and Onychodystrophy A New Variant of Ectodermal Dysplasia

Author Affiliations

From the Departments of Ophthalmology (Drs Font, Schanzer, and Lewis) and Dermatology (Dr Stone), Baylor College of Medicine, Houston.

Arch Ophthalmol. 1986;104(12):1811-1813. doi:10.1001/archopht.1986.01050240085045

• A fourth case of a newly recognized variant of ectodermal dysplasia is reported. This syndrome is characterized by bilateral apocrine hidrocystomas of the eyelid margins, hypodontia, palmar-plantar hyperkeratosis, and onychodystrophy. To our knowledge, this syndrome, with its striking ocular manifestations, has not been previously documented in the ophthalmic literature.