The urachus is a vestigial remnant that, in the midgestational period, connects the umbilicus to the apex of the urinary bladder. Hue and Jacquin1 described the first case of carcinoma arising from the urachal remnant in 1863. More than 200 cases have been subsequently reported. The incidence of urachal malignancy is reported to be less than one in 1000 bladder tumors.2 Patients usually present with urinary symptoms, such as hematuria or dysuria. Histologically, mucin-secreting adenocarcinoma is the most common type of urachal malignant disease.3 Distant metastases, when they occur, usually involve lung or bone; however, metastases to the parieto-occipital3 and occipital lobes of the brain4 have been reported. We describe herein a patient with urachal carcinoma that metastasized to the orbit.
Report of a Case.
In September 1990, a 28-year-old white woman noted recurrent episodes of gross hematuria. Cystoscopy revealed an ulcerating tumor at the
Giordano GG, Shetlar DJ. Orbital Metastasis From a Urachal Tumor. Arch Ophthalmol. 1995;113(4):413-415. doi:10.1001/archopht.1995.01100040027017