Primary liposarcomas occur only rarely in the orbit.1 Liposarcomas can be divided into four distinct histologic types: well differentiated, myxoid, round cell, and pleomorphic, with myxoid being the most common. Twenty-two cases of orbital liposarcoma have been reported in the literature, nine of which were myxoid.1-4 There are no characteristic clinical findings or diagnostic tests that are specific for this tumor. No predilections for sex, location within the orbit, or age have been described, although people with the myxoid type tend to be younger than those with other cell types. The most common presentations are painless proptosis of insidious onset and diplopia. There is only one report of painful proptosis as a primary symptom.4
Report of a Case.
A 45-year-old woman reported the sudden onset of sharp pain and swelling in her medial left lower lid over a 2- to 3-day period. The swelling in her lower
Sabb PC, Syed NA, Sires BS, Lemke BN, Dortzbach RK, Albert DM. Primary Orbital Myxoid Liposarcoma Presenting as Orbital Pain. Arch Ophthalmol. 1996;114(3):353-354. doi:10.1001/archopht.1996.01100130349027