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February 1968

Alveolar Soft-Part Sarcoma of the Orbit

Author Affiliations

New Haven, Conn
From the Department of Surgery, Section of Ophthalmology, Laboratory of Ophthalmic Pathology and the Department of Pathology, Yale University School of Medicine, New Haven, Conn.

Arch Ophthalmol. 1968;79(2):185-188. doi:10.1001/archopht.1968.03850040187016

ALVEOLAR LVEOLAR soft-part sarcoma is a primary malignant neoplasm that very rarely occurs in the orbit. The present report concerns a histologically proven case of alveolar soft-part sarcoma in a patient presenting with unilateral exophthalmos.

Report of a Case 

Clinical History.  —A 55-year-old white factory worker was first seen on March 8, 1966, complaining of a red right eye of approximately three weeks' duration. The patient's family history was noncontributory. His medical history revealed prior episodes of pneumonia, liver disease, traumatic fracture of vertebrae, and a chronic excess ethanol intake. The patient, a poor historian, stated that the right eye had been quite red and was somewhat larger for several weeks (Fig 1). He was unaware of the proptosis until questioned about it. At the time of examination, the patient's visual acuity was 20/20 in each eye without correction. Exophthalmometer readings revealed 28 mm on the right side and 22

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