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Article
June 1969

Juvenile Xanthogranuloma of the Ciliary Body in an Adult

Author Affiliations

St. Louis
From the Department of Ophthalmology, Washington University School of Medicine, St. Louis.

Arch Ophthalmol. 1969;81(6):813-814. doi:10.1001/archopht.1969.00990010815011
Abstract

FOR MORE than 50 years, juvenile xanthogranuloma (JXG) has been recognized as a rare skin disease characteristically occurring in infants and young children.1 It manifests itself as benign, pink, raised lesions of the skin which often regresses spontaneously.

Ocular manifestations may occur concomitantly, or more rarely without the skin lesions.1,2 The ocular manifestations include lesions of the lids, conjunctiva, anterior uveal tract, or orbit.3 The iris lesion is the most important, having been well recognized for over ten years.2 The presenting clinical picture of uveal involvement may be one or more of the following: (1) an asymptomatic localized or diffuse iris tumor, (2) unilateral glaucoma, (3) spontaneous hyphema, (4) a red eye with signs of uveitis, or (5) congenital or acquired heterchromia iridis.

The present case is of interest because: (1) it represents the oldest known patient with this disease, (2) it presented clinically as a

References
1.
Zimmerman, L.E.:  Ocular Lesions in Juvenile Xanthogranuloma (Nevoxanthoendothelioma) , Trans Amer Acad Ophthal Otolaryng 69:412-442 ( (May-June) ) 1965.
2.
Sanders, T.E.:  Intraocular Juvenile Xanthogranuloma (Nevoxantho-endothelioma): A Survey of 20 Cases , Amer J Ophthal 53:455-462 ( (March) ) 1962.
3.
Sanders, T.E.:  Infantile Xanthogranuloma of the Orbit: A Report of Three Cases , Amer J Ophthal 61:1299-1306 ( (May) ) 1966.
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