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Clinical Note
January 2000

Microangiopathy of the Inner Ear, Retina, and Brain (Susac Syndrome)Report of a Case

Author Affiliations

From the Departments of Ears, Nose, and Throat (Drs Ayache, Plouin-Gaudon, and Elbaz) and Neurology (Drs Bakouche and Gout), Fondation Adolphe de Rothschild, Paris, France.

Arch Otolaryngol Head Neck Surg. 2000;126(1):82-84. doi:10.1001/archotol.126.1.82

Microangiopathy of the inner ear, retina, and brain was first described in 1979 by John O. Susac. Since then, approximately 60 cases have been reported. Otolaryngologists must be aware of this syndrome, in which cochleovestibular symptoms are an important part of the diagnosis. In this article, we report a new case of Susac syndrome and discuss the diagnosis, physiopathologic characteristics, and treatment of this disease.