We report a case of von Hippel–Lindau disease in a 55-year-old woman who presented with an intracanalicular hemangioblastoma and discuss the otologic manifestations of this disease. A review of the literature revealed no previous reports of this entity originating in the internal acoustic canal.
Resto VA, Lustig LR. Hemangioblastoma of the Internal Acoustic Canal in a Patient With von Hippel–Lindau DiseaseA Case Report and Review of the Literature. Arch Otolaryngol Head Neck Surg. 2000;126(1):85-88. doi:10.1001/archotol.126.1.85