Polyotia is an extremely rare congenital anomaly of the external ear. While 5 cases have been documented in the literature, only one case of isolated polyotia has been reported to date. We present a case of isolated polyotia in which a child's right auricle was duplicated as a mirror image. The duplicated portion of the affected ear was positioned anteriorly and was approximately the same size as the normal ear. There were 2 fully developed helices, antihelices, and conchae. There was one partially developed tragus and a single narrow external auditory meatus. There were no other congenital anomalies and the child was developmentally normal.
Bajaj Y, Sahni JK, Jain A, Kansal Y. Polyotia. Arch Otolaryngol Head Neck Surg. 2001;127(1):75–77. doi:10.1001/archotol.127.1.75