R. NICKBRYANMDS. JAMESZINREICHMD
A 2-YEAR-OLD white girl with a history of neurofibromatosis type 1 (NF-1) and rhabdomyosarcoma of the right temporal bone presented with a 4-week history of right facial nerve paralysis and ataxic gait. Prior radiographic studies revealed multiple neurofibromas, including involvement of the ipsilateral fallopian canal in the proximal mastoid segment (Figure 1, arrow), but no involvement of the internal auditory canal (Figure 2). The rhabdomyosarcoma had been treated with chemotherapy according to the Intergroup Rhabdomyosarcoma Study IV protocol, regimen 45 (vincristine, actinomycin, and cyclophosphamide), for 1 year. Radiation therapy was not performed because of the mother's concerns regarding adverse effects.
Lehman DA, Mancuso AA, Antonelli PJ. Quiz Case. Arch Otolaryngol Head Neck Surg. 2001;127(3):331. doi:10.1001/archotol.127.3.331