A 4-year-old child had facial palsy of four days' duration. A diagnosis of rhabdomyosarcoma was made from biopsy of an aural polyp. This was followed by radiotherapy and chemotherapy; however, the patient died seven months later.
At autopsy the tumor extended from the internal auditory meatus through the cerebellopontine angle, compressing the fourth ventricle. No distant metastases were found.
Temporal bone sections showed tumor filling the epitympanum, extending along the facial nerve into the internal auditory canal and basal turn of the cochlea, thus accounting for the facial palsy and hearing loss.
El-Gothamy B, Fujita S, Hayden RC. Rhabdomyosarcoma—A Temporal Bone Report. Arch Otolaryngol. 1973;98(2):106–110. doi:10.1001/archotol.1973.00780020112009