This case is reported for the purpose of adding to the literature on lipodystrophy an example which demonstrates that the areas affected need not conform to the original description of Barraquer and Simmons. Their conception of the disorder was that it characteristically involves the face, neck and shoulder girdle and occasionally more or less of the trunk. In cases described subsequently, the involvement conformed to this distribution till in 1939 Bigler1 reported the case of an 18 year old girl which satisfied all the diagnostic criteria except that the loss of subcutaneous fat was confined to the legs, below the knees. Since then there have been reported a few other cases in which the lower extremities solely were involved.
REPORT OF A CASE
The patient was a 5½ year old girl, whose progress was normal in all respects till she reached the age of 1 year. A photograph of
PATTON EF. LIPODYSTROPHY WITH INVOLVEMENT RESTRICTED TO THE FOUR EXTREMITIES. Am J Dis Child. 1945;70(1):31. doi:10.1001/archpedi.1945.02020190038007