Case Reports
August 1945


Am J Dis Child. 1945;70(2):114-NP. doi:10.1001/archpedi.1945.02020200056007

This case of pseudosclerosis is reported because there seems to be considerable confusion in the literature concerning pseudosclerosis, Wilson's disease (progressive lenticular degeneration) and similar conditions. The history and the physical examination in this case reveal such close conformity to the disease entity of pseudosclerosis as described by Westphal1 and Strümpell2 and the disease is so extremely rare3 that this case is considered of great interest.

REPORT OF A CASE  History.—G. S., a 14½ year old girl, was brought to my office on March 24, 1945. Early in 1944 her teacher reported a weakness of the child's right hand. During the summer the child's speech became thicker and she complained frequently of headaches. In Setpember 1944 a staggering gait and jerky movements of the extremities developed. A roentgenogram of the skull was taken at that time and was reported to show no abnormality. A diagnosis of

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